*4.1.5 Outcomes*

No single procedure has been shown to be superior to other in terms of longterm outcomes, and up to 90% patients will have relatively normal bowel function following repair. Although results tend to be quite favorable, one significant cause of significant morbidity and mortality is Hirschsprung's enterocolitis. While the exact etiology of this entity is unknown, bacterial overgrowth and translocation appear to be implicated. Patients present with fever, abdominal distention and diarrhea. Management consists of fluid resuscitation, IV antibiotics and rectal irrigation. Refractory cases require surgical decompression with a proximal ostomy. Other complications such as anastomotic leak, stricture, abscess, wound infection and obstruction occur in up to 10% cases [1].
