**Abstract**

Sacrococcygeal teratomas (SCT) represents a group tumors deriving from the primordial germ cells. It is the most common tumor affecting neonates, with a female to male ratio of almost 4:1.78. SCT are either benign (mature) or malignant (immature) with different outcome. With advancements in ultrasonography, more SCT are diagnosed prenatally. magnetic resonance imaging (MRI) is more accurate in describing the intrapelvic and abdominal extent of the tumor. Most fetal teratomas could be managed by planned delivery and postnatal surgery. The earlier the diagnosis and surgical intervention, the better the prognosis. A complete surgical excision of the tumor is necessary, including coccygectomy, to prevent recurrence. At the time of birth, most lesions are benign and surgical resection can be accomplished with relatively low morbidity and mortality. Recurrence is reported as 2–35% in patients with immature teratomas, tumor spillage, incomplete resection or failure to remove the coccyx. A long-term follow-up is required for any urinary or bowel dysfunction.

**Keywords:** sacrococcygeal, teratomas, surgery, children, tumor
