**6.2. Signs and symptoms**

Young patients often present with syncope, arrhythmia, cardiac arrest, or sudden death. The diagnosis of ARVC should be considered in:


An accurate diagnosis of ARVC is important due to the high risk of drug-resistant arrhythmias and sudden cardiac death. The diagnosis can be established by myocardial biopsy, which shows adipocytes and fibrous tissue. However, these changes can be localised and may not be present at the exact site of biopsy. The availability of cardiac MRI and the gadolinium enhancement techniques are now fundamental in diagnosing ARVC eliminating the need for biopsies.
