**Meet the editors**

Dr. Stavros Hatzopoulos is a faculty member of the Audiology & ENT Clinic, University of Ferrara, Italy, since 1994. He has a background in biomedical, engineering, audiological engineering, and hearing science. He received his BS degree from the University of Southern California, MSc degree from the Texas A&M University, and PhD degree from the Worcester Polytechnic

Institute, Massachusetts. He received his habilitation degree as an associate professor in 2014. He is the author of more than 195 book chapters, peer-reviewed papers, and congress oral presentations. He participated in numerous European-concerted action projects in the areas of otoacoustic emissions, genetics, and nanotechnologies. Currently, he serves as the editor of the portal on otoacoustic emissions (www.otoemissions.org) and the audiology section editor of the *Journal of Hearing Science*.

Dr. Andrea Ciorba is a member of the Audiology & ENT Clinic, University of Ferrara, Italy, since 2004. After completing his degree in Medicine in 1999 and diploma in Otolaryngology and Head and Neck Surgery in October 2003, he obtained his PhD degree in Audiology in March 2008. He is the author of about 120 peer-reviewed papers and book chapters. He is an

editorial board member of peer-reviewed journals. His clinical interests are audiology and vestibology.

Contents

**Preface VII**

**Section 1 Hearing Loss and Its Etiology 1**

Chapter 2 **Genetic Basis of Hearing Loss 25**

Kenichi Takano

Agnieszka Pollak and Monika Ołdak

Chapter 4 **Characterization of Hearing Loss in Children with**

**Section 2 Early Diagnosis and Prevention of Hearing Loss 93**

**Paradigm for Different Etiologies 95**

Chapter 7 **Hearing Screening around the World 113**

Chapter 6 **Hearing Loss at High Frequencies and Oxidative Stress: A New**

Tenório Lins Carnaúba and Pedro de Lemos Menezes

Piotr Henryk Skarżyński and Maciej Ludwikowski

Chapter 3 **Hearing Loss in Congenital Microtia 47**

**Mucopolysaccharidosis 55**

Gasperini and Rossella Parini

Chapter 5 **Sudden Sensorineural Hearing Loss 71**

Chapter 1 **Effects of Genetic Background on Susceptibility and the Acceleration of Hearing Loss in Mice 3**

Shumpei P. Yasuda, Yuki Miyasaka and Yoshiaki Kikkawa

Diego Zanetti, Margherita Vezzani, Federica Di Berardino, Serena

Harun Acıpayam, Hasan Emre Koçak and Mustafa Suphi Elbistanlı

Klinger Vagner Teixeira da Costa, Kelly Cristina Lira de Andrade, Maria Eduarda di Cavalcanti, Ana Claudia Figueiredo Frizzo, Aline
