**1. Introduction**

Takayasu arteritis is a rare vasculitis with no clear etiology presented most of the time in young women. It is even more rare to be presented in children. The clinical characteristics of the disease can be very unspecific and make it harder to diagnose. The diagnosis is done through image criteria along with several clinical data. Treatment is described as multiple options depending on severity and availability. It is important to know the characteristics of this large-vessel vasculitis to be able to identify and treat these patients as soon as possible, the severity and prognosis can vary depending on gender, age, and ethnicity, having a worse prognosis in younger children and African patients. This chapter talks about the characteristics of this disease and how it can be different in adult patients compared to pediatrics.
