**7. Arrhythmogenic right ventricular cardiomyopathy**

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare myocardial disorder inherited in an autosomal dominant pattern with an estimated prevalence of 1:1000–1:5000 [40]. It has been identified as a cause of SCD following sports participation in approximately 4% of cases [5–7]. Cardiomyopathic changes most frequently involve the right ventricular myocardium; however, cases involving the LV have also been reported. Exercise may be important in eliciting ventricular arrhythmias. The usual presenting symptoms are palpitations, syncope, or aborted cardiac arrest. Congestive heart failure may occur in the late stages. T-wave inversion in the right chest leads, indicative of repolarization abnormalities are seen in the ECG. However, the ECG is not sensitive in detecting ARVC [41]. The diagnosis is largely based on major and minor criteria in the echocardiographic and MRI studies, reviewed elsewhere [40, 42]. The mechanism for SCD following exercise is the development of ventricular arrhythmia 40].
