**9. Summary**

Ebstein's malformation is a condition that results from failure of the septal and inferior leaflets of the tricuspid valve to delaminate from the myocardial wall of the right ventricle which in turn results in the hinge point of the tricuspid valve being located within the right ventricle and not at the annulus. Furthermore, there is variability in the extent to which this failure to delaminate has on the heart. The effects may be limited when this anomaly is mild, but in hearts with more severe Ebstein's anomalies, the rotational appearance of the hinge point of the tricuspid valve is more evident. The clinical presentations vary widely secondary to the abnormal morphology and the tricuspid valve and right ventricle as well as the associated heart defects. Neonatal Ebstein's anomaly is continuous to be challenging. With the improvement in diagnostic methods, surgical treatment, and pre and postoperative care, the patients with a severe form of Ebstein's anomaly still have a chance to undergo two-ventricle repair with good long-term outcomes.
