**8. Conclusion**

PN is one of the possible neurologic manifestations encountered by physicians in AAV. Therefore, it is important to take a detailed medical history and examination and adequate investigations to assess for an underlying systemic vasculitis that may be associated with the neuropathy. Mononeuritis multiplex is the most common features of PN in the AAV. The electrodiagnostic studies and nerve biopsy may help in the diagnosis of the disease and PN. When the PN precedes the diagnosis of vasculitis, the medical history and biologic test, especially ANCA test, are vital for diagnosis, but its absence does not exclude the disease. PN in AAV carries a prognostic factor because of the potential risk for motor complications. Therefore, rapid treatment with corticosteroids and immunosuppressant agents is almost warranted in all patients, especially in severe cases. Continuous follow-up of PN in AAV is essential because of frequent relapses.
